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Letter to the Editor: Coexistence of Autoimmune Lymphoproliferative Syndrome and Familial Mediterranean Fever

Sultan Aydin Koker; Nesrin Gulez; Frederic Rieux-Laucat; Ferah Genel; Canan Vergin; Capucine Picard

Volume 17, Issue 2 , June 2020, , Pages 172-174

https://doi.org/10.22034/iji.2020.85774.1725

Abstract
  Autoimmune lymphoproliferative syndrome (ALPS) is a rare inherited disorder of apoptosis, most commonly due to mutations in the FAS (TNFRSF6) gene. ALPS caused by defective lymphocyte homeostasis is characterized by non-malignant lymphoproliferation that often improves with age and is an autoimmune disease, ...  Read More